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1.中国中医科学院研究生院,北京市东城区东直门内南小街16号,100700
2.中国中医科学院西苑医院血液科
3.中国中医科学院西苑医院检验科
Received:14 February 2025,
Revised:2025-05-19,
Published:17 July 2025
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王子淳,陈卓,王德秀等.基因突变对不同中医证型骨髓增生异常综合征患者含砷中药复方治疗疗效的影响[J].中医杂志,2025,66(14):1463-1472.
WANG Zichun,CHEN Zhuo,WANG Dexiu,et al.Influence of Gene Mutation on the Effectiveness of Arsenic-Containing Herbal Compound Formula in Treatment of Myelodysplastic Syndromes of Different TCM Patterns[J].Journal of Traditional Chinese Medicine,2025,66(14):1463-1472.
王子淳,陈卓,王德秀等.基因突变对不同中医证型骨髓增生异常综合征患者含砷中药复方治疗疗效的影响[J].中医杂志,2025,66(14):1463-1472. DOI: 10.13288/j.11-2166/r.2025.14.010.
WANG Zichun,CHEN Zhuo,WANG Dexiu,et al.Influence of Gene Mutation on the Effectiveness of Arsenic-Containing Herbal Compound Formula in Treatment of Myelodysplastic Syndromes of Different TCM Patterns[J].Journal of Traditional Chinese Medicine,2025,66(14):1463-1472. DOI: 10.13288/j.11-2166/r.2025.14.010.
目的
2
探讨基因突变对不同中医证型骨髓增生异常综合征(MDS)患者接受含砷中药复方治疗疗效的影响,为含砷中药复方治疗MDS的临床应用提供依据。
方法
2
回顾性收集接受含砷中药复方治疗的233例MDS患者的临床资料,包括患者的一般情况、中医辨证分型、实验室检查指标、疾病分型、临床疗效。基于中医四诊信息,将患者分为脾肾两虚证和气阴两虚证,再根据第二代测序(NGS)检测结果将其分别分为伴基因突变人群和无基因突变人群。比较两种中医证型不同治疗结局患者的一般资料与疾病特征,分析基因突变对不同中医证型患者临床疗效的影响,并对伴基因突变MDS患者的有效率影响因素进行多因素Logistic回归分析。
结果
2
共纳入脾肾两虚型组190例(伴基因突变的119例)、气阴两虚型组43例(伴基因突变的23例)。脾肾两虚型组与气阴两虚型组患者疗效评价、总有效率和总反应率差异均无统计学意义(
P
>0.05)。脾肾两虚型组中,伴基因突变的患者总有效率为65.55%(78/119)低于不伴基因突变患者的80.28%(57/71),差异有统计学意义(
P
=0.033);疗效评价和总反应率差异无统计学意义(
P
>0.05)。气阴两虚型组中,是否伴基因突变患者疗效评估、总有效率、总反应率比较差异均无统计学(
P
>0.05)。伴基因突变的脾肾两虚型组患者中治疗无效人群伴复杂核型率高于治疗有效人群(
P
=0.031)、CBL基因突变率亦高于治疗有效人群(
P
=0.032),而治疗有效人群中DDX41基因突变率较治疗无效人群高(
P
=0.033),其他基因突变及年龄、性别分布及基因突变数目、骨髓增生活跃程度、原始细胞区间、是否存在网状纤维组织增生、染色体预后等级比较在有效人群和无效人群中差异无统计学意义(
P
>0.05)。伴基因突变的气阴两虚型组患者不同治疗结局人群间比较,各项目差异均无统计学意义(
P
>0.05)。多因素Logistic回归分析显示,复杂核型、CBL突变、DDX41突变为脾肾两虚证伴基因突变MDS有效率的独立影响因素(
P
<0.05),其中DDX41突变是脾肾两虚型组的独立保护因素(
OR
>1),而复杂核型、CBL突变则是独立危险因素(
OR
<1)。
结论
2
含砷中药复方治疗不伴基因突变的脾肾两虚型组MDS的疗效较好,在脾肾两虚型组患者中含砷中药复方治疗不伴复杂核型、CBL突变和伴DDX41突变的基因突变MDS有效率较高,且DDX41突变是脾肾两虚型组患者含砷中药复方治疗有效的独立保护因素,而复杂核型、CBL突变则是独立危险因素。在气阴两虚型患者中,基因突变相关因素对含砷中药复方疗效未见显著影响。
Objective
2
To observe the effect of gene mutation on the effectiveness of arsenic-containing Chinese herbal compound formulas in the treatment of myelodysplastic syndromes (MDS) of different traditional Chinese medicine (TCM) patterns, so as to provide the basis for the clinical application.
Methods
2
Clinical data of 442 MDS patients who were treated with arsenic-containing herbal compound formulas were retrospectively collected, including the baseline demographic and clinical characteristics of the patients. Based on the TCM four examinations, the patients were divided into the spleen-kidney deficiency group as well as the qi-yin deficiency group, and according to the results of the next-generation sequencing (NGS) test, they were divided into the group with and without gene mutation respectively. The influence of gene mutation on the clinical effectiveness of patients with different TCM patterns was analyzed, the baseline demographic and clinical characteristics of the patients with different outcomes of the two TCM patterns were compared, and multivariate Logistic regression analysis was conducted on the influencing factors of the effective rate of MDS patients with gene mutation.
Results
2
A total of 190 cases were included in the spleen-kidney deficiency group (119 cases with gene mutation) and 43 cases in the
qi
-
yin
deficiency group (23 cases with gene mutation). No statistically significant differences were noted in effectiveness assessment, total effective rate, and total response rate between the spleen-kidney deficiency group and the
qi
-
yin
deficiency group (
P
>0.05). In the spleen-kidney deficiency group, the total effective rate of MDS with gene mutation was 65.55% (78/119), which was lower than 80.28% (57/71) of MDS without gene mutation, with statistical significance (
P
= 0.033), while no statistical differences in effectiveness assessment and total response rate were noted (
P
>0.05). In the
qi
-
yin
deficiency group, no statistical differences were observed in effectiveness assessment, total effective rate, and total response rate of the patients in with or without gene mutation (
P
>0.05). In the spleen-kidney deficiency group with gene mutation, the rate of complex karyotype (
P
= 0.031) and the mutation rate of CBL gene (
P
= 0.032) in the ineffective population were higher than those in the effective population, while the mutation rate of DDX41 gene in the effective population was higher than that in the ineffective population (
P
= 0.033). No statistically significant differences were found in other gene mutation
s, age, gender distribution, number of gene mutations, bone marrow hyperplasia degree, blast cell range, reticular fiber tissue proliferation or not, and prognosis of chromosomal abnormalities between the effective and ineffective populations (
P
>0.05). In the
qi
-
yin
deficiency group with gene mutation, no statistically significant differences were found in various items between populations with different outcomes (
P
>0.05). Multivariate Logistic regression analysis showed that complex karyotype, CBL mutation, and DDX41 mutation were independently associated with the effective rate of MDS with spleen-kidney deficiency and gene mutation (
P
<0.05). DDX41 mutation was an independent protective factor in the spleen-kidney deficiency group (
OR
>1), while complex karyotype and CBL mutation were independent risk factors (
OR
<1).
Conclusion
2
The arsenic-containing TCM compound formulas exhibited better effectiveness in MDS with spleen-kidney deficiency pattern without mutation; and in MDS with spleen-kidney deficiency pattern without complex karyotypes, CBL mutation, and with DDX41 mutations. Furthermore, DDX41 mutation was an independent protective factor in the spleen-kidney deficiency group, while complex karyotype and CBL mutation were independent risk factors. In MDS with
qi
-
yin
deficiency pattern, gene mutation-related factors showed no significant impact on the effectiveness of arsenic-containing TCM compound formulas.
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